Search results for " Periventricular"

showing 4 items of 4 documents

Congenital emphysematous lung disease associated with a novel Filamin A mutation. Case report and literature review

2019

Abstract Background Progressive lung involvement in Filamin A (FLNA)-related cerebral periventricular nodular heterotopia (PVNH) has been reported in a limited number of cases. Case presentation We report a new pathogenic FLNA gene variant (c.7391_7403del; p.Val2464Alafs*5) in a male infant who developed progressive lung disease with emphysematous lesions and interstitial involvement. Following lobar resection, chronic respiratory failure ensued necessitating continuous mechanical ventilation and tracheostomy. Cerebral periventricular nodular heterotopia was also present. Conclusions We report a novel variant of the FLNA gene, associated with a severe lung disorder and PNVH. The lung disord…

Lung DiseasesMalePathologymedicine.medical_specialtyFilaminsmedicine.medical_treatmentChildren; Congenital enphysema; Filamin a; Lung disease; Periventricular nodular heterotopiaCase ReportFilaminKeywords: Filamin a Congenital enphysema Lung disease Children Periventricular nodular heterotopiaFilamin aLung Disorder03 medical and health sciences0302 clinical medicineNeuroimagingLoss of Function Mutation030225 pediatricsmedicineHumansFLNA030212 general & internal medicineLungChildrenCongenital enphysemaGenetic testingMechanical ventilationLungmedicine.diagnostic_testbusiness.industrylcsh:RJ1-570BrainInfantlcsh:Pediatricsrespiratory systemRespiration ArtificialPeriventricular nodular heterotopiamedicine.anatomical_structurePulmonary EmphysemaRespiratory failureLung diseasePediatrics Perinatology and Child HealthRadiography ThoracicRespiratory InsufficiencyTomography X-Ray ComputedbusinessBMC Pediatrics
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The main sequelae of preterm birth: Focus on neurodevelopmental disorders

2018

Preterm birth is a traumatic event that interrupts the physiological processes that allow the development of the Nervous System and the body systems, resulting in a multi-organ dysfunction, of an entity in inverse proportion to the gestational age, which causes respiratory, cardiovascular, metabolic, infectious endocrine problems. and neurological. In particular, at a neurological level, in the most serious cases, for macroscopic lesions of the Central Nervous System, there is the risk of incurring in evolutionary Disabilities (Infantile Cerebral Palsy etc.); but in the absence of severe damage, since the birth occurs at a critical moment of the cerebral development in which the cortex is b…

Periventricular leukomalaciaMedicine (all)Preterm birthNeonatal Intensive Care Unit; Periventricular leukomalacia; Preterm birth;Neonatal Intensive Care Unit
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Hypoproteinemia on the first day of life and adverse outcome in very preterm infants admitted to the neonatal intensive care unit

2012

International audience; OBJECTIVE: We aimed to investigate the relationship between day-1 hypoproteinemia and severe adverse outcome (SAO) in very preterm infants admitted to the neonatal intensive care unit (NICU). STUDY DESIGN: Retrospective study of all patients born from 24 to 31 weeks gestation and cared for in our NICU over an 8-year period. Infants were excluded if the serum protein value on the first day of life was not available. RESULT: A total of 913 patients were included. In all, 14.6% presented with SAO (death or severe neurological injury on cranial ultrasound). Hypoproteinemia (total protein level \textless40 g l(-1)) on day 1 of life occurred in 19.5 % of all patients. The …

MalePediatricsmedicine.medical_specialtyNeonatal intensive care unitAdverse outcomesLeukomalacia PeriventricularBirth weightDay of lifeMEDLINE[ SDV.MHEP.PED ] Life Sciences [q-bio]/Human health and pathology/PediatricsDiseasesInfant Premature Diseases03 medical and health sciencesHypoproteinemia0302 clinical medicineIntensive Care Units Neonatal030225 pediatricsNeonatalMedicineBirth WeightHumans030212 general & internal medicinePrematureCerebral HemorrhageHypoproteinemia[SDV.MHEP.PED]Life Sciences [q-bio]/Human health and pathology/PediatricsPeriventricularbusiness.industryInfant NewbornObstetrics and GynecologyInfantBlood Proteinsmedicine.diseaseNewbornInfant newborn3. Good healthVery pretermIntensive Care UnitsPediatrics Perinatology and Child HealthFemalebusinessInfant PrematureLeukomalacia
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Battered child syndrome: cerebral ultrasound and CT findings after vigorous shaking.

1992

Child abuse by whiplash-shaking can lead to severe cerebral damage, neurological defects and mental retardation. Cerebral damage has been found with and without external evidence of head injury. We report the sonographic findings in two children after traumatization due to repetitive vigorous whiplash shaking. Cerebral sonography revealed cerebral edema at admission or within 48 hours thereafter. Follow-up studies demonstrated development of marked brain atrophy in both cases. The sonographic findings were confirmed by cranial computerized tomography. Doppler sonography was used to monitor cerebral perfusion by measuring intracranial blood flow. The clinical history of the patients demonstr…

Child abuseMalemedicine.medical_specialtyIntracranial PressureLeukomalacia PeriventricularBrain EdemaCerebral edemaHead Injuries ClosedBattered Child SyndromemedicineWhiplashBattered Child SyndromeHumansCerebral perfusion pressureIntracranial pressureNeurologic Examinationmedicine.diagnostic_testbusiness.industryHead injuryInfant NewbornInfantGeneral Medicinemedicine.diseaseEchoencephalographySurgeryEchoencephalographyPediatrics Perinatology and Child HealthFemaleNeurology (clinical)RadiologybusinessTomography X-Ray ComputedNeuropediatrics
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